Chronic Respiratory Disease: 

The similarities and differences between pleuroparenchymal fibroelastosis and idiopathic pulmonary fibrosis

Chronic Respiratory Disease, Volume 16, Issue , January-December 2019. The idiopathic form of pleuroparenchymal fibroelastosis (PPFE) is categorized as a rare idiopathic interstitial pneumonia in the current classification. The majority of PPFE cases are idiopathic, but many predisposing factors or comorbidities have been reported. Although histological PPFE is predominantly located in the upper lobes, which are less often affected by fibrosis in patients with idiopathic pulmonary fibrosis (IPF),...

SAGE Publications Ltd STM: Chronic Respiratory Disease: Table of Contents

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